|
楼主 |
发表于 2008-12-9 16:08:31
|
显示全部楼层
75-8-第八节 预 后
本病为慢性进行性血管病变,疾病具有一定间歇性进展和缓解的倾向。国外报道5年生存率83%-94%不等。早期的炎性指标和系统症状往往在发病几年后逐渐被血管缺血的症状所替代。个别病人可自行缓解,多数患者疾病处于长期慢性进展中,但是早期诊断、免疫抑制剂的使用和积极的外科治疗可使预后明显改善。日本的一组1000例患者长期随访的结果显示仅有25%的患者出现明显的并发症。心脏的并发症包括充血性心功能不全和缺血性心脏病为主要的致死原因。北京阜外医院对530例大动脉炎的随访结果显示,在平均8.2年的随访期中死亡55例,其中死于脑出血13例,手术并发症4例,肾功能不全4例,心功能不全3例,急性心肌梗死 3例,脑血栓 2例,动脉瘤破裂2例,其他24例。5 }$ Z) y5 [; b/ ^6 j; R3 `; R- {
(薛 静 赵 岩)3 X$ z' l7 t$ h0 o; X7 L9 ~( j
参考文献:
; _- m6 a6 j; s, Q( _3 \: ~
& [3 A+ w6 H- q# e 郑德裕,昊遐,刘庆红等.大动脉炎200例的临床分析心脏血管疾病,1973, 3:43.
8 |- x" ]% L, i! I" k f. t1 F
. d A! d) R$ j; U- v Hirose H, Takagi M, Miyagawa N, et al. Genetic risk fac-tor for abdominal aortic aneurysm: HLA-DR2. A JapanesesItudy. J Vase Surg, 1998,27:500 2 v4 B# {9 q/ I1 K
/ R; P5 s; X$ E% i9 f% p8 [
Rizzi R,Bruno S, Stellacci C et al. Takayasu's arteritis,acell mediated large-vessel vasculitis. Int J Clin Lab Res, 1999,29:8 " A5 o9 p' I' l" b/ r
8 j! c8 P* |' k& }7 d Marina N. Pathogenesis of Takayasu's arteritis. J Nephrol,2001,14:506* I' n0 _+ f5 G' g5 p! e7 }( N) b4 H
6 d% x: r7 `6 b Kasuya K, Hashimoto Y, Numano F. Left ventricular dys-functon and HLA-Bw52 antigen in Takayasu arteritis. Heart Ves-sels, 1992,7:116 2 N2 E; X9 b% D2 u9 i
' t: H) Y P2 Q/ @- o5 r+ B/ W Kerr GS, Hallahan CW, Giordano J, et al. Takayasu's ar-teritis. Ann Intern Med, 1994,120:919 . J% y( }; @/ O0 p+ r# @, P. R
0 D& l; p# j! n6 O Lupi-Herrera E, Sanchez-Torres G, Marcushamer J, et al.Takayasu' s arteritis: Clinical study of 107 cases. Am Heart J,1977,93:94 8 |$ Y* W6 j1 G: |: |
' d9 c/ h) G3 l+ ]
Sharma S, Kamalaka RT, Rajani M, et al. The incidenceand patterns of pumonary involvement in Takayasu arteritis. ClinRadiol, 1990, 42:177
' _3 o' g; M" V6 [- O$ }+ m q+ N
- W; |) h, W. U- `2 v, o: J: n* C+ C Enzo A, Angelo V, Massimo V,et al. The role of radiologyin the diagnosis and management of Takayasu’s arteritis. JNephrol,2001,14:514
% K" g+ J3 ]7 ]% r0 J) n+ B+ a4 {; S9 X7 P; o, G- |: G
Sima D, Thiele B, Turowski A, et al. Anti-endothelial anti-bodies in Takayasu's arteritis. Arthritis Rheum, 1994, 37:441 3 X$ G& a9 L. R8 L, m- y
/ l% f$ v% t7 I" _; ^
Maria G S, Enrica B, Elena B, et al. Takayasu's arteritis:therapeutic strategies. J Nephrol, 2001,14:525 5 T. d1 c: K9 a6 W3 i' {9 Q# `
) T/ {) V9 ^6 P) z
Zheng D, Fan D, Liu L. Takayasu arteritis in China: A re-port of 530 cases. Heart Vessels 1992, (Suppl) 7:3675 |
|