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发表于 2008-12-10 09:58:40
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67-10-第十节 预 后
随着免疫抑制治疗的出现,特发性炎性肌病的预后不断改善。皮质激素出现前成人特发性炎性肌病的5年生存率为60%,1947一1968年为 68%,近几年为 80 。用通信方式对1986一1998年的59例特发性炎性肌病病人进行了随访,一年生存率为90%,2-5年生存率为80%。前5年共死亡12例,其中死于肺内感染5例,肺纤维化4例,肿瘤3例。发病前3年病情较重,激素用量大,激素减量或停用时病情易复发;发病5年后病情趋于稳定,有三分之一的病人脱离激素,病情仍保持稳定。我们的病人多数较重,病例也较少,因此,这些统计数字与实际情况可能会有差异,它只是在一定程度上也反映了一种趋向。除使用免疫抑制剂外,早诊断早治疗,以及有效控制并发症也有助于预后的改善。
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